Dentinogenesis imperfecta - Type II: Case report

Abstract

Dentinogenesis imperfecta or hereditary opalescent dentin is a rare hereditary disorder charac- terized by defective dentin forma- tion, resulting in color changes in the affected teeth and early enamel loss, causing rapid attri- tion and decrease of the vertical dimension. A case is reported, in which the patient presented the typical clinical signs and roent- genographic manifestations of dentinogenesis imperfecta in all permanent teeth, with no evidence of bone alterations, thus eliminat- ing the possibility of osteogenesis imperfecta association and leading to type II classification. Key words: dentinogenesis imperfecta, hereditary opalescent dentin.