Dentinogenesis imperfecta Type II or hereditary opalescent dentin: literature review and case report

Abstract

The authors present a litera- ture review and a case report of dentinogenesis imperfecta type II, in a 20-year-old pale derm patient, with esthetic deficiency in permanent teething. Clinically, teeth shouved a yellowish-brown coloration accompanied by enamel fracture, with uncommon contours and smaller coronary dimension in gingival-occlusal direction. It was found the occurrence of similar cases in the family, proving the hereditariness. Radiographically, the absence of osseous implication and the complete obliteration of the pulp chambers, due to disordered production of modified dentin, were observed. The treatment consists, basically, in the protection of the tooth structures, with the use of crowns, overdentures or interoc- clusal protection with bite-plates for nocturne use. Key words: dentinogenesis imperfecta, hereditary opalescent dentin, dentin alteration, dentino- genesis imperfecta type II, domi- nant autosomal alteration.