ODONTOGENIC KERATOCYST IN THE MAXILLA: CASE REPORT
DOI:
https://doi.org/10.5335/rfo.v28i1.14204Keywords:
Cisto Odontogênico, Síndrome de Gorlin-Goltz, Odontologia HospitalarAbstract
OJECTIVE: To report the process of diagnosis and treatment of an odontogenic keratocyst (QO) in the maxillary sinus and its importance in the investigation and diagnosis of Gorlin-Goltz Syndrome (GGS). CASE REPORT: A 20-year-old female patient presented at the Dentistry and Stomatology service, referred by the Medical Genetics team to investigate the presence of QO to define the diagnosis of GGS. The patient had only two criteria for the diagnosis of GGS, the diagnosis of multiple basal cell carcinomas (major criterion) and macrocephaly (minor criterion), and therefore, if the presence of OC was detected, GGS would be confirmed. Panoramic radiography was performed and the presence of alterations in the bone trabeculae in the maxillary tuberosity on the left side was verified. For this reason, computed tomography of the maxillary sinuses was also requested and a well-defined lesion was found, occupying almost completely the left maxillary sinus in close contact with the root of tooth 27. Therefore, an incisional biopsy of the lesion was performed, accompanied by puncture of the same. In the puncture, a characteristic caseous content suggestive of keratin was obtained. The histopathological report of the lesion was described by the pathologist as an odontogenic cyst. With this, tooth extraction procedures for tooth 27 and enucleation of the lesion in the maxillary sinus were carried out by the dentistry and otorhinolaryngology teams, respectively, in a surgical center. The histopathological report confirmed the presence of QO, so it was possible to confirm the diagnosis of GGS by the medical genetics team. The patient showed no signs of recurrence or new QO after 2 years of the procedure. FINAL CONSIDERATIONS: GGS requires special dental attention, given the high rate of QO in patients with this syndrome. A thorough dental examination involving clinical examination and radiographic examinations should be performed at follow-up visits.
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